224th ENMC International Workshop:
2017; Elsevier BV; Volume: 28; Issue: 1 Linguagem: Inglês
10.1016/j.nmd.2017.09.016
ISSN1873-2364
AutoresYves Allenbach, Andrew L. Mammen, Olivier Benveniste, Werner Stenzel, Yves Allenbach, Anthony A. Amato, Audrey Aussey, Olivier Benveniste, Jan De Bleecker, Ingrid de Groot, Marjolein Visser, Hans H. Goebel, B. Hervier, Norina Fischer, David Hilton‐Jones, Janine A. Lamb, Ingrid E. Lundberg, Andrew L. Mammen, Tahseen Mozaffar, Ichizo Nishino, Alan Pestronk, Ulrike Schara, Werner Stenzelr,
Tópico(s)Immunodeficiency and Autoimmune Disorders
Resumo•Three distinct subtypes of immune-mediated necrotizing myopathies are defined.•New pathological criteria for immune-mediated necrotizing myopathies are defined.•Anti-HMGCR myopathy, anti-SRP myopathy and antibody negative IMNM are defined.•Therapeutic recommendations for anti-HMGCR myopathy, anti-SRP myopathy are given.
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