Artigo Acesso aberto Revisado por pares

224th ENMC International Workshop:

2017; Elsevier BV; Volume: 28; Issue: 1 Linguagem: Inglês

10.1016/j.nmd.2017.09.016

ISSN

1873-2364

Autores

Yves Allenbach, Andrew L. Mammen, Olivier Benveniste, Werner Stenzel, Yves Allenbach, Anthony A. Amato, Audrey Aussey, Olivier Benveniste, Jan De Bleecker, Ingrid de Groot, Marjolein Visser, Hans H. Goebel, B. Hervier, Norina Fischer, David Hilton‐Jones, Janine A. Lamb, Ingrid E. Lundberg, Andrew L. Mammen, Tahseen Mozaffar, Ichizo Nishino, Alan Pestronk, Ulrike Schara, Werner Stenzelr,

Tópico(s)

Immunodeficiency and Autoimmune Disorders

Resumo

•Three distinct subtypes of immune-mediated necrotizing myopathies are defined.•New pathological criteria for immune-mediated necrotizing myopathies are defined.•Anti-HMGCR myopathy, anti-SRP myopathy and antibody negative IMNM are defined.•Therapeutic recommendations for anti-HMGCR myopathy, anti-SRP myopathy are given.

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