
Idiopathic interstitial pneumonias: review of the latest American Thoracic Society/European Respiratory Society classification
2018; Colégio Brasileiro de Radiologia e Diagnóstico por Imagem; Volume: 51; Issue: 5 Linguagem: Inglês
10.1590/0100-3984.2016.0134
ISSN1678-7099
AutoresDaniel Simões Oliveira, José de Arimatéia Araújo Filho, Antônio Fernando Lins de Paiva, Eduardo Seigo Ikari, Rodrigo Caruso Chate, César Higa Nomura,
Tópico(s)Occupational and environmental lung diseases
ResumoThe diagnosis of idiopathic interstitial pneumonias (IIPs) involves a multidisciplinary scenario in which the radiologist assumes a key role. The latest (2013) update of the IIP classification by the American Thoracic Society/European Respiratory Society proposed some important changes to the original classification of 2002. The novelties include the addition of a new disease (idiopathic pleuroparenchymal fibroelastosis) and the subdivision of the IIPs into four main groups: chronic fibrosing IIPs (idiopathic pulmonary fibrosis and nonspecific interstitial pneumonia); smoking-related IIPs (desquamative interstitial pneumonia and respiratory bronchiolitis-associated interstitial lung disease); acute or subacute IIPs (cryptogenic organizing pneumonia and acute interstitial pneumonia); rare IIPs (lymphoid interstitial pneumonia and idiopathic pleuroparenchymal fibroelastosis); and the so-called "unclassifiable" IIPs. In this study, we review the main clinical, tomographic, and pathological characteristics of each IIP.
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