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Extraskeletal Mesenchymal Chondrosarcoma

2018; American Medical Association; Volume: 142; Issue: 11 Linguagem: Inglês

10.5858/arpa.2017-0109-rs

1543-2165

Komal Arora, Nicole D. Riddle,

Oral and Maxillofacial Pathology

Extraskeletal mesenchymal chondrosarcoma is a rare soft tissue sarcoma arising from soft tissues, mainly of the lower extremities, meninges, and orbits. It usually presents during the second to third decades of life, and has a slight predominance in females. Histologically, it has a typical biphasic pattern comprising small cells and islands of hyaline cartilage. It can pose a diagnostic challenge in small biopsy specimens where 1 of the 2 components can be absent. The prognosis is extremely variable; survival varies depending on the location of the tumor.