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Morbihan Syndrome, a UK Case Series

2020; Lippincott Williams & Wilkins; Volume: 36; Issue: 5 Linguagem: Inglês

10.1097/iop.0000000000001589

1537-2677

Camille Yvon, Hardeep Singh Mudhar, Tessa Fayers, We Fong Siah, Raman Malhotra, Zanna Currie, Jennifer Tan, Saul Rajak,

Ophthalmology and Eye Disorders

Purpose: To describe 10 patients with Morbihan syndrome, a rare condition characterized by the slow appearance of erythema and solid edema on the upper portion of the face, and review the literature. Methods: Retrospective case series and review. Results: The majority of patients were male (80%), and the mean age at presentation was 67 years (range, 48–88 years); 60% had asymmetrical disease (affecting mainly the right side). All subjects underwent a lid biopsy to support the diagnosis of Morbihan syndrome, which showed features of inflammation and vascular dysfunction, highly suggestive of a rosacea histological picture complicated by chronic lymphoedema. A range of medical and surgical treatment were used with variable success. The most effective ones included oral isotretinoin, intralesional triamcinolone injections, and debulking surgery. Conclusions: Morbihan syndrome is a rare and chronic condition. It can be difficult to treat and may require a range of interventions.