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Kilt Syndrome?

2002; Wiley; Volume: 118; Issue: 4 Linguagem: Inglês

10.1046/j.1365-2141.2002.370311.x

1365-2141

J. Van Der Veen, K.K. Hampton, Michael Makris,

Central Venous Catheters and Hemodialysis

A Scottish group recently reported the association of bilateral deep vein thrombosis (DVT) with absence of the inferior vena cava (IVC) (Chee et al, 2001), confirming the findings of a similar series from Italy (Ruggeri et al, 2001). The authors used a figure of an abdominal computerized tomography (CT) scan from one of their patients to illustrate the absence of the IVC. Although they did not comment on it, an equally striking abnormality on the figure is a hypoplastic left and a hypertrophied right kidney. We recently encountered a similar patient. A 16-year-old girl developed bilateral DVTs while on holiday abroad and a CT scan performed at the time was reported to show an absent IVC and an enlarged right renal mass (Fig 1). This mass was initially interpreted as a possible hypernephroma. Further investigation on her return to the UK, however, showed the right renal mass to be a hypertrophied kidney associated with a grossly hypoplastic left kidney. We feel it is essential that an abdominal CT or magnetic resonance imaging scan should be performed in every case of bilateral DVT in a young person to determine the IVC and renal structures. Abdominal CT scan showing a hypertrophied right kidney, a grossly hypoplastic left kidney (short arrow) and an absent inferior vena cava (normal position indicated by the long arrow). In view of the kidney and IVC abnormalities with leg thromboses, an appropriate name for this condition could be KILT syndrome.