Portal de Periódicos da CAPES

Perirenal Lymphangiomatosis

2014; Korean Society for Sexual Medicine and Andrology; Volume: 32; Issue: 2 Linguagem: Inglês

10.5534/wjmh.2014.32.2.116

2287-4690

Tae Gyeong Jeon, Do Hoon Kong, Hyun Jun Park, Suk Kim, Won Young Park, Soo Dong Kim, Hong Koo Ha,

Vascular anomalies and interventions

Lymphangioma is a rare, benign mesenchymal neoplasm, which is characterized by numerous intercommunicating cystic spaces containing lymphatic fluid. It is considered a congenital disease resulting from the obstruction of regional lymph drainage during the developmental period. Lymphangioma may be focal/unilateral or diffuse/bilateral, and in the latter case, it is referred to as lymphangiomatosis. Here, we report a case of a 38-year-old man with perirenal lymphangiomatosis. The patient's chief complaint was left flank pain, and left pleural effusion was found on radiological examination. After radical nephrectomy, the pathological examinations revealed that the kidney was enclosed by a multicystic mass with intrarenal cystic dilatations. We report the case and discuss the management of perirenal lymphangiomatosis with a literature review.