Artigo Acesso aberto Revisado por pares

Infantile myofibromatosis

2017; Elsevier BV; Volume: 92; Issue: 6 Linguagem: Inglês

10.1590/abd1806-4841.20175001

ISSN

1806-4841

Autores

Margarita Larralde, Bruno Ferrari, Juan Pablo Martínez, María Angélica Fernández Barbieri, José Méndez, José G Casas,

Tópico(s)

Sarcoma Diagnosis and Treatment

Resumo

Infantile myofibromatosis is a mesenchymal disorder characterized by the fibrous proliferation of the skin, bone, muscle and viscera. It is the most common fibrous tumor in childhood. We present a newborn with skin and bone disease without visceral involvement, who showed good response to vinblastine and methotrexate. Clinical features, etiology, diagnosis, and treatment are reviewed.

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