Produção Nacional
Revisado por pares
Erasmus Syndrome
2022; Radiological Society of North America; Volume: 4; Issue: 5 Linguagem: Lituano
10.1148/ryct.220162
ISSN2638-6135
AutoresMaurício Ricardo Moreira da Silva Filho, Juliana Rocha Garcia, Eduardo Kaiser Ururahy Nunes Fonseca, Márcio Valente Yamada Sawamura,
Tópico(s)Peripheral Neuropathies and Disorders
ResumoHomeRadiology: Cardiothoracic ImagingVol. 4, No. 5 PreviousNext Images in Cardiothoracic ImagingFree AccessErasmus SyndromeMauricio Ricardo Moreira da Silva Filho , Juliana Rocha Garcia, Eduardo Kaiser Ururahy Nunes Fonseca, Marcio Valente Yamada SawamuraMauricio Ricardo Moreira da Silva Filho , Juliana Rocha Garcia, Eduardo Kaiser Ururahy Nunes Fonseca, Marcio Valente Yamada SawamuraAuthor AffiliationsFrom the Department of Radiology, Instituto de Radiologia–INRAD, Faculdade de Medicina da Universidade de São Paulo, Travessa da Rua Doutor Ovídio Pires de Campos 75, Portaria 1, Cerqueira César, São Paulo, SP, Brazil 05403-010 (M.R.M.d.S.F., J.R.G., E.K.U.N.F., M.V.Y.S.); and Department of Diagnostic Imaging, Instituto do Coração, Universidade de São Paulo, São Paulo, Brazil (E.K.U.N.F.).Address correspondence to M.R.M.d.S.F. (email: [email protected]).Mauricio Ricardo Moreira da Silva Filho Juliana Rocha GarciaEduardo Kaiser Ururahy Nunes FonsecaMarcio Valente Yamada SawamuraPublished Online:Oct 20 2022https://doi.org/10.1148/ryct.220162MoreSectionsPDF ToolsImage ViewerAdd to favoritesCiteTrack CitationsPermissionsReprints ShareShare onFacebookTwitterLinked In A 48-year-old man who worked as a sandblaster for 10 years was diagnosed with systemic sclerosis according to the 2013 American College of Rheumatology and European League Against Rheumatism classification criteria (1). The association of systemic sclerosis following exposure to silica with or without silicosis is termed Erasmus syndrome, first described in 1957 (2). Clinical features of systemic sclerosis are not uniform and usually include pulmonary and esophageal changes (3), most frequently seen as interstitial lung disease (nonspecific interstitial pneumonia pattern) and esophageal dilation at CT (Figure). Recently, there has been a resurgence of silicosis related to artificial stone workers (4).Unenhanced CT images in a 48-year-old man who worked as a sandblaster for 10 years and was diagnosed with systemic sclerosis. (A) Axial and (B) coronal images in the lung window show basilar symmetrical reticular and ground-glass opacities, with some subpleural sparing. A dilated esophagus can also be noted (black arrow). (C) Maximum intensity projection image exhibits bilateral perilymphatic micronodules, exemplified by the white arrows. (D) Coronal multiplanar reformatted image in the bone window depicts “eggshell” calcified lymphadenopathy (white arrows) in the hilar and mediastinal regions, a finding virtually pathognomonic of silica exposure.Download as PowerPointOpen in Image Viewer Disclosures of conflicts of interest: M.R.M.d.S.F. No relevant relationships. J.R.G. No relevant relationships. E.K.U.N.F. No relevant relationships. M.V.Y.S. No relevant relationships.Keywords: Thorax, Lung, Esophagus, Connective Tissue Disorders, Occupational/Environmental Hazards, CTAuthors declared no funding for this work.References1. van den Hoogen F, Khanna D, Fransen J, et al. 2013 classification criteria for systemic sclerosis: an American College of Rheumatology/European League against Rheumatism collaborative initiative. Arthritis Rheum 2013;65(11):2737–2747. Crossref, Medline, Google Scholar2. Erasmus LD. Scleroderma in goldminers on the Witwatersrand with particular reference to pulmonary manifestations. S Afr J Lab Clin Med 1957;3(3):209–231. Medline, Google Scholar3. Rocha LF, Luppino Assad AP, Marangoni RG, Del Rio AP, Marques-Neto JF, Sampaio-Barros PD. Systemic sclerosis and silica exposure: a rare association in a large Brazilian cohort. Rheumatol Int 2016;36(5):697–702. Crossref, Medline, Google Scholar4. Turner MT, Samuel SR, Silverstone EJ, Yates DH. Silica Exposure and Connective Tissue Disease: An Underrecognized Association in Three Australian Artificial Stone Workers. Am J Respir Crit Care Med 2020;201(3):378–380. Crossref, Medline, Google ScholarArticle HistoryReceived: July 26 2022Revision requested: Sept 13 2022Revision received: Sept 21 2022Accepted: Sept 30 2022Published online: Oct 20 2022 FiguresReferencesRelatedDetailsRecommended Articles RSNA Education Exhibits RSNA Case Collection Vol. 4, No. 5 Metrics Altmetric Score PDF download
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