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BIBTEX RIS

Refractory Thrombotic Thrombocytopenic Purpura in a Patient With Triple X Syndrome

2024; Cureus, Inc.; Linguagem: Inglês

10.7759/cureus.67631

2168-8184

Pedro Arthur da Rocha Ribas, Julia Ghiraldi, Giovanna Gugelmin, Lucas Wagner Görtz, Maurício de Carvalho, Gustavo Lenci Marques,

Platelet Disorders and Treatments

Clinical manifestations of triple X syndrome (karyotype 47, XXX) can include autoimmune diseases. We describe the occurrence of acquired thrombotic thrombocytopenic purpura (TTP), an autoimmune condition, refractory to plasmapheresis and rituximab in a patient with triple X syndrome who required vincristine administration for disease remission. To our knowledge, this rare coexistence is the first of its kind reported in Brazil.