Prune belly syndrome in a neonate with severe bilateral hydronephrosis: A rare case report from Somalia
2024; Elsevier BV; Volume: 123; Linguagem: Inglês
10.1016/j.ijscr.2024.110310
ISSN2210-2612
AutoresAbdirahman Omer Ali, Abdirahman Ibrahim Said, Mohamed Ahmed Abdilahi, Abdirahman Said Deheye, Abdisalam Hassan Muse,
Tópico(s)Pediatric Urology and Nephrology Studies
ResumoPrune belly syndrome (PBS), also known as Eagle-Barret syndrome, is a rare congenital disorder characterized by abdominal wall muscle underdevelopment, urinary system abnormalities, and cryptorchidism. This case report presents the clinical features, diagnosis, and management of PBS in a newborn. This is the first case report of prune belly syndrome in Somalia. The condition is estimated to occur in approximately 1 in 30,000 to 1 in 50,000 live births, making it a relatively uncommon presentation. Recognizing and managing this syndrome is crucial, as it can lead to significant morbidity and mortality if not addressed promptly.
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