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Birt-Hogg-Dubé syndrome

1997; Elsevier BV; Volume: 83; Issue: 4 Linguagem: Inglês

10.1016/s1079-2104(97)90152-9

1528-395X

Nader Nadershahi, William B. Wescott, Barbara M. Egbert,

Medical Imaging and Pathology Studies

Birt-Hogg-Dubé syndrome manifests as small, skin-colored, dome-shaped, or pedunculated cutaneous lesions. Three histopathologic patterns have been described: fibrofolliculomas, trichodiscomas, and acrochordons. The patient described in this article also had small, elevated, intraoral papules involving the mucosal surfaces of the lips, buccal mucosa, and gingivae, which represents a finding that had not been described in the literature previously.